ICD-10 · PDGM grouping
E76 Disorders of glycosaminoglycan metabolism
All 12 codes in the E76 family, with the PDGM clinical group, comorbidity subgroup and primary-position rule CMS assigns, read from the CMS grouper crosswalk v07.2.26 and the CDC FY2027 code file.
Codes in family
12
Can lead a claim
12
Cannot lead a claim
0
What CMS assigns to E76
All 12 codes group to MMTA - Other. None of the 12 is assigned a comorbidity subgroup. Every code can lead a claim.
Every code in E76
Descriptions are CDC’s FY2027 wording; where CMS’s grouper abbreviates one, its form is shown beneath.
| Code | Description | Primary position | Clinical group | Comorbidity subgroup |
|---|---|---|---|---|
| E76.0 Mucopolysaccharidosis, type I | ||||
| E76.01 | Hurler's syndrome | Can lead a claim | A | None |
| E76.02 | Hurler-Scheie syndrome | Can lead a claim | A | None |
| E76.03 | Scheie's syndrome | Can lead a claim | A | None |
| E76.1 | Mucopolysaccharidosis, type II | Can lead a claim | A | None |
| E76.2 Other mucopolysaccharidoses | ||||
| E76.21 Morquio mucopolysaccharidoses | ||||
| E76.210 | Morquio A mucopolysaccharidoses | Can lead a claim | A | None |
| E76.211 | Morquio B mucopolysaccharidoses | Can lead a claim | A | None |
| E76.219 | Morquio mucopolysaccharidoses, unspecified | Can lead a claim | A | None |
| E76.22 | Sanfilippo mucopolysaccharidoses | Can lead a claim | A | None |
| E76.29 | Other mucopolysaccharidoses | Can lead a claim | A | None |
| E76.3 | Mucopolysaccharidosis, unspecified | Can lead a claim | A | None |
| E76.8 | Other disorders of glucosaminoglycan metabolism | Can lead a claim | A | None |
| E76.9 | Glucosaminoglycan metabolism disorder, unspecified | Can lead a claim | A | None |
Sources: CMS HH PPS Grouper Software v07.2.26, effective 2026-10-01, for the clinical group, comorbidity subgroup, code-first conventions and primary-position flags; CDC NCHS ICD-10-CM FY2027 code descriptions for the family title and code wording. This is the crosswalk Medicare runs a claim through. Grouping also depends on admission source, timing, the OASIS functional items and the rest of the diagnosis list.
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