ICD-10 · PDGM grouping
E70 Disorders of aromatic amino-acid metabolism
All 26 codes in the E70 family, with the PDGM clinical group, comorbidity subgroup and primary-position rule CMS assigns, read from the CMS grouper crosswalk v07.2.26 and the CDC FY2027 code file.
Codes in family
26
Can lead a claim
26
Cannot lead a claim
0
What CMS assigns to E70
All 26 codes group to MMTA - Other. None of the 26 is assigned a comorbidity subgroup. Every code can lead a claim.
Every code in E70
Descriptions are CDC’s FY2027 wording; where CMS’s grouper abbreviates one, its form is shown beneath.
| Code | Description | Primary position | Clinical group | Comorbidity subgroup |
|---|---|---|---|---|
| E70.0 | Classical phenylketonuria | Can lead a claim | A | None |
| E70.1 | Other hyperphenylalaninemias | Can lead a claim | A | None |
| E70.2 Disorders of tyrosine metabolism | ||||
| E70.20 | Disorder of tyrosine metabolism, unspecified | Can lead a claim | A | None |
| E70.21 | Tyrosinemia | Can lead a claim | A | None |
| E70.29 | Other disorders of tyrosine metabolism | Can lead a claim | A | None |
| E70.3 Albinism | ||||
| E70.30 | Albinism, unspecified | Can lead a claim | A | None |
| E70.31 Ocular albinism | ||||
| E70.310 | X-linked ocular albinism | Can lead a claim | A | None |
| E70.311 | Autosomal recessive ocular albinism | Can lead a claim | A | None |
| E70.318 | Other ocular albinism | Can lead a claim | A | None |
| E70.319 | Ocular albinism, unspecified | Can lead a claim | A | None |
| E70.32 Oculocutaneous albinism | ||||
| E70.320 | Tyrosinase negative oculocutaneous albinism | Can lead a claim | A | None |
| E70.321 | Tyrosinase positive oculocutaneous albinism | Can lead a claim | A | None |
| E70.328 | Other oculocutaneous albinism | Can lead a claim | A | None |
| E70.329 | Oculocutaneous albinism, unspecified | Can lead a claim | A | None |
| E70.33 Albinism with hematologic abnormality | ||||
| E70.330 | Chediak-Higashi syndrome | Can lead a claim | A | None |
| E70.331 | Hermansky-Pudlak syndrome | Can lead a claim | A | None |
| E70.338 | Other albinism with hematologic abnormality | Can lead a claim | A | None |
| E70.339 | Albinism with hematologic abnormality, unspecified | Can lead a claim | A | None |
| E70.39 | Other specified albinism | Can lead a claim | A | None |
| E70.4 Disorders of histidine metabolism | ||||
| E70.40 | Disorders of histidine metabolism, unspecified | Can lead a claim | A | None |
| E70.41 | Histidinemia | Can lead a claim | A | None |
| E70.49 | Other disorders of histidine metabolism | Can lead a claim | A | None |
| E70.5 | Disorders of tryptophan metabolism | Can lead a claim | A | None |
| E70.8 Other disorders of aromatic amino-acid metabolism | ||||
| E70.81 | Aromatic L-amino acid decarboxylase deficiency | Can lead a claim | A | None |
| E70.89 | Other disorders of aromatic amino-acid metabolism | Can lead a claim | A | None |
| E70.9 | Disorder of aromatic amino-acid metabolism, unspecified | Can lead a claim | A | None |
Sources: CMS HH PPS Grouper Software v07.2.26, effective 2026-10-01, for the clinical group, comorbidity subgroup, code-first conventions and primary-position flags; CDC NCHS ICD-10-CM FY2027 code descriptions for the family title and code wording. This is the crosswalk Medicare runs a claim through. Grouping also depends on admission source, timing, the OASIS functional items and the rest of the diagnosis list.
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