October 1 update. Our PDGM and ICD-10 tools now use the FY2027 code set: 190 codes added, 30 deleted, and no existing code changed clinical group.

See what changed

ICD-10 · PDGM grouping

E70 Disorders of aromatic amino-acid metabolism

All 26 codes in the E70 family, with the PDGM clinical group, comorbidity subgroup and primary-position rule CMS assigns, read from the CMS grouper crosswalk v07.2.26 and the CDC FY2027 code file.

ICD-10-CM FY2027 · CMS grouper v07.2.26

Codes in family

26

Can lead a claim

26

Cannot lead a claim

0

What CMS assigns to E70

All 26 codes group to MMTA - Other. None of the 26 is assigned a comorbidity subgroup. Every code can lead a claim.

Every code in E70

Descriptions are CDC’s FY2027 wording; where CMS’s grouper abbreviates one, its form is shown beneath.

CodeDescriptionPrimary positionClinical groupComorbidity subgroup
E70.0Classical phenylketonuriaCan lead a claimANone
E70.1Other hyperphenylalaninemiasCan lead a claimANone
E70.2 Disorders of tyrosine metabolism
E70.20Disorder of tyrosine metabolism, unspecifiedCan lead a claimANone
E70.21TyrosinemiaCan lead a claimANone
E70.29Other disorders of tyrosine metabolismCan lead a claimANone
E70.3 Albinism
E70.30Albinism, unspecifiedCan lead a claimANone
E70.31 Ocular albinism
E70.310X-linked ocular albinismCan lead a claimANone
E70.311Autosomal recessive ocular albinismCan lead a claimANone
E70.318Other ocular albinismCan lead a claimANone
E70.319Ocular albinism, unspecifiedCan lead a claimANone
E70.32 Oculocutaneous albinism
E70.320Tyrosinase negative oculocutaneous albinismCan lead a claimANone
E70.321Tyrosinase positive oculocutaneous albinismCan lead a claimANone
E70.328Other oculocutaneous albinismCan lead a claimANone
E70.329Oculocutaneous albinism, unspecifiedCan lead a claimANone
E70.33 Albinism with hematologic abnormality
E70.330Chediak-Higashi syndromeCan lead a claimANone
E70.331Hermansky-Pudlak syndromeCan lead a claimANone
E70.338Other albinism with hematologic abnormalityCan lead a claimANone
E70.339Albinism with hematologic abnormality, unspecifiedCan lead a claimANone
E70.39Other specified albinismCan lead a claimANone
E70.4 Disorders of histidine metabolism
E70.40Disorders of histidine metabolism, unspecifiedCan lead a claimANone
E70.41HistidinemiaCan lead a claimANone
E70.49Other disorders of histidine metabolismCan lead a claimANone
E70.5Disorders of tryptophan metabolismCan lead a claimANone
E70.8 Other disorders of aromatic amino-acid metabolism
E70.81Aromatic L-amino acid decarboxylase deficiencyCan lead a claimANone
E70.89Other disorders of aromatic amino-acid metabolismCan lead a claimANone
E70.9Disorder of aromatic amino-acid metabolism, unspecifiedCan lead a claimANone

Sources: CMS HH PPS Grouper Software v07.2.26, effective 2026-10-01, for the clinical group, comorbidity subgroup, code-first conventions and primary-position flags; CDC NCHS ICD-10-CM FY2027 code descriptions for the family title and code wording. This is the crosswalk Medicare runs a claim through. Grouping also depends on admission source, timing, the OASIS functional items and the rest of the diagnosis list.

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