ICD-10 · PDGM grouping
Q20-Q28 — Congenital malformations of the circulatory system
Every ICD-10-CM code in this range and the PDGM clinical group CMS assigns to it, read from the CMS grouper crosswalk v07.2.26.
Codes in range
102
No clinical group
9
A period cannot be grouped from these.
Barred as primary
0
CMS rejects these in the primary position.
Where these codes group
93 of the 102 codes in Q20-Q28 group to MMTA - Other. A further 9 are assigned no clinical group at all, which means a 30-day period cannot be grouped from them.
Code families in Q20-Q28
One page per three-character family: every code in it, whether it can lead a claim, its clinical group and comorbidity subgroup.
- Q20Congenital malformations of cardiac chambers and connections9 codes
- Q21Congenital malformations of cardiac septa17 codes
- Q22Congenital malformations of pulmonary and tricuspid valves9 codes
- Q23Congenital malformations of aortic and mitral valves9 codes
- Q24Other congenital malformations of heart9 codes
- Q25Congenital malformations of great arteries22 codes
- Q26Congenital malformations of great veins9 codes
- Q27Other congenital malformations of peripheral vascular system12 codes
- Q28Other congenital malformations of circulatory system6 codes
Every code in Q20-Q28
Descriptions are CMS’s own, abbreviated as CMS abbreviates them.
| Code | Description | Clinical group | Primary position |
|---|---|---|---|
| Q200 | Common arterial trunk | A | Can lead a claim |
| Q201 | Double outlet right ventricle | A | Can lead a claim |
| Q202 | Double outlet left ventricle | A | Can lead a claim |
| Q203 | Discordant ventriculoarterial connection | A | Can lead a claim |
| Q204 | Double inlet ventricle | A | Can lead a claim |
| Q205 | Discordant atrioventricular connection | A | Can lead a claim |
| Q206 | Isomerism of atrial appendages | A | Can lead a claim |
| Q208 | Oth congenital malform of cardiac chambers and connections | A | Can lead a claim |
| Q209 | Congenital malform of cardiac chambers and connections, unsp | None | Cannot lead a claim |
| Q210 | Ventricular septal defect | A | Can lead a claim |
| Q2110 | Atrial septal defect, unspecified | A | Can lead a claim |
| Q2111 | Secundum atrial septal defect | A | Can lead a claim |
| Q2112 | Patent foramen ovale | A | Can lead a claim |
| Q2113 | Coronary sinus atrial septal defect | A | Can lead a claim |
| Q2114 | Superior sinus venosus atrial septal defect | A | Can lead a claim |
| Q2115 | Inferior sinus venosus atrial septal defect | A | Can lead a claim |
| Q2116 | Sinus venosus atrial septal defect, unspecified | A | Can lead a claim |
| Q2119 | Other specified atrial septal defect | A | Can lead a claim |
| Q2120 | Atrioventricular septal defect, unsp as to part or complete | A | Can lead a claim |
| Q2121 | Partial atrioventricular septal defect | A | Can lead a claim |
| Q2122 | Transitional atrioventricular septal defect | A | Can lead a claim |
| Q2123 | Complete atrioventricular septal defect | A | Can lead a claim |
| Q213 | Tetralogy of Fallot | A | Can lead a claim |
| Q214 | Aortopulmonary septal defect | A | Can lead a claim |
| Q218 | Other congenital malformations of cardiac septa | A | Can lead a claim |
| Q219 | Congenital malformation of cardiac septum, unspecified | None | Cannot lead a claim |
| Q220 | Pulmonary valve atresia | A | Can lead a claim |
| Q221 | Congenital pulmonary valve stenosis | A | Can lead a claim |
| Q222 | Congenital pulmonary valve insufficiency | A | Can lead a claim |
| Q223 | Other congenital malformations of pulmonary valve | A | Can lead a claim |
| Q224 | Congenital tricuspid stenosis | A | Can lead a claim |
| Q225 | Ebstein's anomaly | A | Can lead a claim |
| Q226 | Hypoplastic right heart syndrome | A | Can lead a claim |
| Q228 | Other congenital malformations of tricuspid valve | A | Can lead a claim |
| Q229 | Congenital malformation of tricuspid valve, unspecified | A | Can lead a claim |
| Q230 | Congenital stenosis of aortic valve | A | Can lead a claim |
| Q231 | Congenital insufficiency of aortic valve | A | Can lead a claim |
| Q232 | Congenital mitral stenosis | A | Can lead a claim |
| Q233 | Congenital mitral insufficiency | A | Can lead a claim |
| Q234 | Hypoplastic left heart syndrome | A | Can lead a claim |
| Q2381 | Bicuspid aortic valve | A | Can lead a claim |
| Q2382 | Congenital mitral valve cleft leaflet | A | Can lead a claim |
| Q2388 | Other congenital malformations of aortic and mitral valves | A | Can lead a claim |
| Q239 | Congenital malformation of aortic and mitral valves, unsp | None | Cannot lead a claim |
| Q240 | Dextrocardia | A | Can lead a claim |
| Q241 | Levocardia | A | Can lead a claim |
| Q242 | Cor triatriatum | A | Can lead a claim |
| Q243 | Pulmonary infundibular stenosis | A | Can lead a claim |
| Q244 | Congenital subaortic stenosis | A | Can lead a claim |
| Q245 | Malformation of coronary vessels | A | Can lead a claim |
| Q246 | Congenital heart block | A | Can lead a claim |
| Q248 | Other specified congenital malformations of heart | A | Can lead a claim |
| Q249 | Congenital malformation of heart, unspecified | None | Cannot lead a claim |
| Q250 | Patent ductus arteriosus | A | Can lead a claim |
| Q251 | Coarctation of aorta | A | Can lead a claim |
| Q2521 | Interruption of aortic arch | A | Can lead a claim |
| Q2529 | Other atresia of aorta | A | Can lead a claim |
| Q253 | Supravalvular aortic stenosis | A | Can lead a claim |
| Q2540 | Congenital malformation of aorta unspecified | None | Cannot lead a claim |
| Q2541 | Absence and aplasia of aorta | A | Can lead a claim |
| Q2542 | Hypoplasia of aorta | A | Can lead a claim |
| Q2543 | Congenital aneurysm of aorta | A | Can lead a claim |
| Q2544 | Congenital dilation of aorta | A | Can lead a claim |
| Q2545 | Double aortic arch | A | Can lead a claim |
| Q2546 | Tortuous aortic arch | A | Can lead a claim |
| Q2547 | Right aortic arch | A | Can lead a claim |
| Q2548 | Anomalous origin of subclavian artery | A | Can lead a claim |
| Q2549 | Other congenital malformations of aorta | A | Can lead a claim |
| Q255 | Atresia of pulmonary artery | A | Can lead a claim |
| Q256 | Stenosis of pulmonary artery | A | Can lead a claim |
| Q2571 | Coarctation of pulmonary artery | A | Can lead a claim |
| Q2572 | Congenital pulmonary arteriovenous malformation | A | Can lead a claim |
| Q2579 | Other congenital malformations of pulmonary artery | A | Can lead a claim |
| Q258 | Other congenital malformations of other great arteries | A | Can lead a claim |
| Q259 | Congenital malformation of great arteries, unspecified | None | Cannot lead a claim |
| Q260 | Congenital stenosis of vena cava | A | Can lead a claim |
| Q261 | Persistent left superior vena cava | A | Can lead a claim |
| Q262 | Total anomalous pulmonary venous connection | A | Can lead a claim |
| Q263 | Partial anomalous pulmonary venous connection | A | Can lead a claim |
| Q264 | Anomalous pulmonary venous connection, unspecified | A | Can lead a claim |
| Q265 | Anomalous portal venous connection | A | Can lead a claim |
| Q266 | Portal vein-hepatic artery fistula | A | Can lead a claim |
| Q268 | Other congenital malformations of great veins | A | Can lead a claim |
| Q269 | Congenital malformation of great vein, unspecified | A | Can lead a claim |
| Q270 | Congenital absence and hypoplasia of umbilical artery | A | Can lead a claim |
| Q271 | Congenital renal artery stenosis | A | Can lead a claim |
| Q272 | Other congenital malformations of renal artery | A | Can lead a claim |
| Q2730 | Arteriovenous malformation, site unspecified | None | Cannot lead a claim |
| Q2731 | Arteriovenous malformation of vessel of upper limb | A | Can lead a claim |
| Q2732 | Arteriovenous malformation of vessel of lower limb | A | Can lead a claim |
| Q2733 | Arteriovenous malformation of digestive system vessel | A | Can lead a claim |
| Q2734 | Arteriovenous malformation of renal vessel | A | Can lead a claim |
| Q2739 | Arteriovenous malformation, other site | A | Can lead a claim |
| Q274 | Congenital phlebectasia | A | Can lead a claim |
| Q278 | Oth congenital malformations of peripheral vascular system | A | Can lead a claim |
| Q279 | Congenital malformation of peripheral vascular system, unsp | None | Cannot lead a claim |
| Q280 | Arteriovenous malformation of precerebral vessels | A | Can lead a claim |
| Q281 | Other malformations of precerebral vessels | A | Can lead a claim |
| Q282 | Arteriovenous malformation of cerebral vessels | A | Can lead a claim |
| Q283 | Other malformations of cerebral vessels | A | Can lead a claim |
| Q288 | Oth congenital malformations of circulatory system | A | Can lead a claim |
| Q289 | Congenital malformation of circulatory system, unspecified | None | Cannot lead a claim |
Source: CMS HH PPS Grouper Software v07.2.26, effective 2026-10-01. This is the crosswalk Medicare runs a claim through. Grouping also depends on admission source, timing, the OASIS functional items and the rest of the diagnosis list.
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