ICD-10 · PDGM grouping
E74 Other disorders of carbohydrate metabolism
All 24 codes in the E74 family, with the PDGM clinical group, comorbidity subgroup and primary-position rule CMS assigns, read from the CMS grouper crosswalk v07.2.26 and the CDC FY2027 code file.
Codes in family
24
Can lead a claim
23
Cannot lead a claim
1
What CMS assigns to E74
23 of the 24 codes group to MMTA - Other; 1 is assigned no clinical group. None of the 24 is assigned a comorbidity subgroup. 23 of the 24 can lead a claim.
Every code in E74
Descriptions are CDC’s FY2027 wording; where CMS’s grouper abbreviates one, its form is shown beneath.
| Code | Description | Primary position | Clinical group | Comorbidity subgroup |
|---|---|---|---|---|
| E74.0 Glycogen storage disease | ||||
| E74.00 | Glycogen storage disease, unspecified | Can lead a claim | A | None |
| E74.01 | von Gierke disease | Can lead a claim | A | None |
| E74.02 | Pompe disease | Can lead a claim | A | None |
| E74.03 | Cori disease | Can lead a claim | A | None |
| E74.04 | McArdle disease | Can lead a claim | A | None |
| E74.05 | Lysosome-associated membrane protein 2 [LAMP2] deficiency | Can lead a claim | A | None |
| E74.09 | Other glycogen storage disease | Can lead a claim | A | None |
| E74.1 Disorders of fructose metabolism | ||||
| E74.10 | Disorder of fructose metabolism, unspecified | Can lead a claim | A | None |
| E74.11 | Essential fructosuria | Can lead a claim | A | None |
| E74.12 | Hereditary fructose intolerance | Can lead a claim | A | None |
| E74.19 | Other disorders of fructose metabolism | Can lead a claim | A | None |
| E74.2 Disorders of galactose metabolism | ||||
| E74.20 | Disorders of galactose metabolism, unspecified | Can lead a claim | A | None |
| E74.21 | Galactosemia | Can lead a claim | A | None |
| E74.29 | Other disorders of galactose metabolism | Can lead a claim | A | None |
| E74.3 Other disorders of intestinal carbohydrate absorption | ||||
| E74.31 | Sucrase-isomaltase deficiency | Can lead a claim | A | None |
| E74.39 | Other disorders of intestinal carbohydrate absorption | Can lead a claim | A | None |
| E74.4 | Disorders of pyruvate metabolism and gluconeogenesis | Can lead a claim | A | None |
| E74.8 Other specified disorders of carbohydrate metabolism | ||||
| E74.81 Disorders of glucose transport, not elsewhere classified | ||||
| E74.810 | Glucose transporter protein type 1 deficiency | Can lead a claim | A | None |
| E74.818 | Other disorders of glucose transport | Can lead a claim | A | None |
| E74.819 | Disorders of glucose transport, unspecified | Can lead a claim | A | None |
| E74.82 Disorders of citrate metabolism | ||||
| E74.820 | SLC13A5 Citrate Transporter Disorder | Can lead a claim | A | None |
| E74.829 | Other disorders of citrate metabolism | Can lead a claim | A | None |
| E74.89 | Other specified disorders of carbohydrate metabolism | Can lead a claim | A | None |
| E74.9 | Disorder of carbohydrate metabolism, unspecified | Cannot lead a claimPrincipal diagnosis not assigned to a clinical group | None | None |
Sources: CMS HH PPS Grouper Software v07.2.26, effective 2026-10-01, for the clinical group, comorbidity subgroup, code-first conventions and primary-position flags; CDC NCHS ICD-10-CM FY2027 code descriptions for the family title and code wording. This is the crosswalk Medicare runs a claim through. Grouping also depends on admission source, timing, the OASIS functional items and the rest of the diagnosis list.
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