ICD-10 · PDGM grouping
Q80-Q89 — Other congenital malformations
Every ICD-10-CM code in this range and the PDGM clinical group CMS assigns to it, read from the CMS grouper crosswalk v07.2.26.
Codes in range
82
No clinical group
18
A period cannot be grouped from these.
Barred as primary
0
CMS rejects these in the primary position.
Where these codes group
57 of the 82 codes in Q80-Q89 group to MMTA - Other, but the range is not uniform — it spreads across 3 clinical groups. A further 18 are assigned no clinical group at all, which means a 30-day period cannot be grouped from them.
Code families in Q80-Q89
One page per three-character family: every code in it, whether it can lead a claim, its clinical group and comorbidity subgroup.
- Q80Congenital ichthyosis7 codes
- Q81Epidermolysis bullosa5 codes
- Q82Other congenital malformations of skin9 codes
- Q83Congenital malformations of breast6 codes
- Q84Other congenital malformations of integument9 codes
- Q85Phakomatoses, not elsewhere classified11 codes
- Q86Congenital malformation syndromes due to known exogenous causes, not elsewhere classified4 codes
- Q87Other specified congenital malformation syndromes affecting multiple systems21 codes
- Q89Other congenital malformations, not elsewhere classified10 codes
Every code in Q80-Q89
Descriptions are CMS’s own, abbreviated as CMS abbreviates them.
| Code | Description | Clinical group | Primary position |
|---|---|---|---|
| Q800 | Ichthyosis vulgaris | None | Cannot lead a claim |
| Q801 | X-linked ichthyosis | None | Cannot lead a claim |
| Q802 | Lamellar ichthyosis | None | Cannot lead a claim |
| Q803 | Congenital bullous ichthyosiform erythroderma | None | Cannot lead a claim |
| Q804 | Harlequin fetus | None | Cannot lead a claim |
| Q808 | Other congenital ichthyosis | None | Cannot lead a claim |
| Q809 | Congenital ichthyosis, unspecified | None | Cannot lead a claim |
| Q810 | Epidermolysis bullosa simplex | A | Can lead a claim |
| Q811 | Epidermolysis bullosa letalis | A | Can lead a claim |
| Q812 | Epidermolysis bullosa dystrophica | A | Can lead a claim |
| Q818 | Other epidermolysis bullosa | A | Can lead a claim |
| Q819 | Epidermolysis bullosa, unspecified | None | Cannot lead a claim |
| Q820 | Hereditary lymphedema | C | Can lead a claim |
| Q821 | Xeroderma pigmentosum | A | Can lead a claim |
| Q822 | Congenital cutaneous mastocytosis | A | Can lead a claim |
| Q823 | Incontinentia pigmenti | A | Can lead a claim |
| Q824 | Ectodermal dysplasia (anhidrotic) | A | Can lead a claim |
| Q825 | Congenital non-neoplastic nevus | A | Can lead a claim |
| Q826 | Congenital sacral dimple | A | Can lead a claim |
| Q828 | Other specified congenital malformations of skin | A | Can lead a claim |
| Q829 | Congenital malformation of skin, unspecified | None | Cannot lead a claim |
| Q830 | Congenital absence of breast with absent nipple | A | Can lead a claim |
| Q831 | Accessory breast | A | Can lead a claim |
| Q832 | Absent nipple | A | Can lead a claim |
| Q833 | Accessory nipple | A | Can lead a claim |
| Q838 | Other congenital malformations of breast | A | Can lead a claim |
| Q839 | Congenital malformation of breast, unspecified | None | Cannot lead a claim |
| Q840 | Congenital alopecia | A | Can lead a claim |
| Q841 | Congenital morphological disturbances of hair, NEC | None | Cannot lead a claim |
| Q842 | Other congenital malformations of hair | None | Cannot lead a claim |
| Q843 | Anonychia | None | Cannot lead a claim |
| Q844 | Congenital leukonychia | None | Cannot lead a claim |
| Q845 | Enlarged and hypertrophic nails | None | Cannot lead a claim |
| Q846 | Other congenital malformations of nails | None | Cannot lead a claim |
| Q848 | Other specified congenital malformations of integument | A | Can lead a claim |
| Q849 | Congenital malformation of integument, unspecified | None | Cannot lead a claim |
| Q8500 | Neurofibromatosis, unspecified | B | Can lead a claim |
| Q8501 | Neurofibromatosis, type 1 | B | Can lead a claim |
| Q8502 | Neurofibromatosis, type 2 | B | Can lead a claim |
| Q8503 | Schwannomatosis | B | Can lead a claim |
| Q8509 | Other neurofibromatosis | B | Can lead a claim |
| Q851 | Tuberous sclerosis | A | Can lead a claim |
| Q8581 | PTEN hamartoma tumor syndrome | A | Can lead a claim |
| Q8582 | Other Cowden syndrome | A | Can lead a claim |
| Q8583 | Von Hippel-Lindau syndrome | A | Can lead a claim |
| Q8589 | Other phakomatoses, not elsewhere classified | A | Can lead a claim |
| Q859 | Phakomatosis, unspecified | A | Can lead a claim |
| Q860 | Fetal alcohol syndrome (dysmorphic) | A | Can lead a claim |
| Q861 | Fetal hydantoin syndrome | A | Can lead a claim |
| Q862 | Dysmorphism due to warfarin | A | Can lead a claim |
| Q868 | Oth congen malform syndromes due to known exogenous causes | A | Can lead a claim |
| Q870 | Congen malform syndromes predom affecting facial appearance | A | Can lead a claim |
| Q8711 | Prader-Willi syndrome | A | Can lead a claim |
| Q8719 | Other congen malform synd predom assoc with short stature | A | Can lead a claim |
| Q872 | Congenital malformation syndromes predom involving limbs | A | Can lead a claim |
| Q873 | Congenital malformation syndromes involving early overgrowth | A | Can lead a claim |
| Q8740 | Marfan syndrome, unspecified | A | Can lead a claim |
| Q87410 | Marfan syndrome with aortic dilation | A | Can lead a claim |
| Q87418 | Marfan syndrome with other cardiovascular manifestations | A | Can lead a claim |
| Q8742 | Marfan syndrome with ocular manifestations | A | Can lead a claim |
| Q8743 | Marfan syndrome with skeletal manifestation | A | Can lead a claim |
| Q875 | Oth congenital malformation syndromes w oth skeletal changes | A | Can lead a claim |
| Q8781 | Alport syndrome | A | Can lead a claim |
| Q8782 | Arterial tortuosity syndrome | A | Can lead a claim |
| Q8783 | Bardet-Biedl syndrome | A | Can lead a claim |
| Q8784 | Laurence-Moon syndrome | A | Can lead a claim |
| Q8785 | MED13L syndrome | A | Can lead a claim |
| Q8786 | Kleefstra syndrome | A | Can lead a claim |
| Q8787 | Hao-Fountain Syndrome | A | Can lead a claim |
| Q8788 | CTNNB1 syndrome | B | Can lead a claim |
| Q8789 | Oth congenital malformation syndromes, NEC | A | Can lead a claim |
| Q87A | Loeys-Dietz syndrome | A | Can lead a claim |
| Q8901 | Asplenia (congenital) | A | Can lead a claim |
| Q8909 | Congenital malformations of spleen | A | Can lead a claim |
| Q891 | Congenital malformations of adrenal gland | A | Can lead a claim |
| Q892 | Congenital malformations of other endocrine glands | A | Can lead a claim |
| Q893 | Situs inversus | A | Can lead a claim |
| Q894 | Conjoined twins | A | Can lead a claim |
| Q897 | Multiple congenital malformations, not elsewhere classified | A | Can lead a claim |
| Q8981 | Kabuki syndrome | A | Can lead a claim |
| Q8989 | Other specified congenital malformations | A | Can lead a claim |
| Q899 | Congenital malformation, unspecified | None | Cannot lead a claim |
Source: CMS HH PPS Grouper Software v07.2.26, effective 2026-10-01. This is the crosswalk Medicare runs a claim through. Grouping also depends on admission source, timing, the OASIS functional items and the rest of the diagnosis list.
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